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Sézary's disease



Sézary's disease
Classification & external resources
ICD-10 C84.1
ICD-9 202.2
ICD-O: M9701/3
DiseasesDB 8595
MeSH D012751

Sézary's disease (or "Sézary syndrome") is a type of cutaneous lymphoma characterized by Albert Sézary.[1]

"Sézary's cells" are T-cells that have pathological quantities of mucopolysaccharides.

Sézary's disease is sometimes considered a late stage of mycosis fungoides.

Additional recommended knowledge

Contents

General

Sezary syndrome and Mycosis Fungoides are T-cell lymphomas whose primary manifestation is in the skin.

Etiology

HTLV has thought to have been associated with both of the above cutaneous mycoses.

Symptoms

The hallmark symptoms for Sezary Syndrome are (1) Generalized erythroderma (2)Lymphadenopathy, and (3) Atypical T-cells ("Sezary cells") in the peripheral blood.

Treatment

Vorinostat (Zolinza®) is a second-line drug for CTCL. Treatments are often used in combination.

References

  1. ^ synd/3594 at Who Named It
  • 584056846 at GPnotebook
 
This article is licensed under the GNU Free Documentation License. It uses material from the Wikipedia article "Sézary's_disease". A list of authors is available in Wikipedia.
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