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Trigonocephaly



Trigonocephaly
Classification & external resources
ICD-10 Q75.0
ICD-9 756.0
DiseasesDB 33252

Trigonocephaly is a type of cephalic disorder. This is the premature fusion of the metopic suture (part of the frontal suture which joins the two halves of the frontal bone of the skull) in which a V-shaped abnormality occurs at the front of the skull. It is characterized by the triangular prominence of the forehead and closely set eyes. Genetic testing may be offered to determine the cause and recurrence risk.

Treatment

Surgery can greatly reduce the visual effects of trigonocephaly. It can also help address comorbid elevated intracranial pressure.[1]

History

It is believed that the first surgery to correct the disorder was successfully completed in early 1962 in San Diego, California, on a six-month-old girl.[2]

References

  1. ^ Shimoji T, Tomiyama N (2004). "Mild trigonocephaly and intracranial pressure: report of 56 patients". Childs Nerv Syst 20 (10): 749–56. doi:10.1007/s00381-004-0970-y. PMID 15185114.
  2. ^ Anerson FM, Gwinn JL, Todt JC (1962). "Trigonocephaly. Identity and surgical treatment". J. Neurosurg. 19: 723–30. PMID 13861226.
 
This article is licensed under the GNU Free Documentation License. It uses material from the Wikipedia article "Trigonocephaly". A list of authors is available in Wikipedia.
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