Classification & external resources
| Anterior (frontal) view of the opened heart. White arrows indicate normal blood flow. (Tricuspid valve labeled at bottom left.)
Tricuspid atresia is a form of congenital heart disease whereby there is a complete absence of the tricuspid valve. Therefore, there is an absence of right atrioventricular connection. This leads to a hypoplastic or an absence of the right ventricle.
This defect is contracted during prenatal development, when the heart does not finish developing. It causes the heart to be unable to properly oxigenate the rest of the blood in the body. Because of this, the body does not have enough oxygen to live, and steps must be taken to keep the child alive.
Because of the lack of an A-V connection, an atrial septal defect (ASD) must be present to maintain blood flow. Also, since there is a lack of a right ventricle there must be a way to pump blood into the pulmonary arteries, and this is accomplished by a ventricular septal defect (VSD).
Additional recommended knowledge
Blood is mixed in the left atrium. Because the only way the pulmonary circulation receives blood is through the VSD, a patent ductus arteriosus is usually also formed to increase pulmonary flow.
- progressive cyanosis
- poor feeding
- tachypnea over the first 2 weeks of life
- holosystolic murmur due to the VSD
- superior axis and left ventricular hypertrophy (since it must pump blood to both the pulmonary and systemic systems)
- normal heart size
- Tricuspid Atresia information from Seattle Children's Hospital Heart Center
|Congenital malformations and deformations of circulatory system (Q20-Q28, 745-747)|
|Cardiac chambers and connections||Persistent truncus arteriosus - Double outlet right ventricle (Taussig-Bing syndrome) - Transposition of the great vessels (dextro, levo)|
|Cardiac septa||Ventricular septal defect - Atrial septal defect (Lutembacher's syndrome) - Atrioventricular septal defect (Ostium primum) - Tetralogy of Fallot - Eisenmenger's syndrome|
|Right: pulmonary and tricuspid valves||pulmonary valves (stenosis, insufficiency) - tricuspid valves (stenosis, atresia) - Ebstein's anomaly|
|Left: aortic and mitral valves||aortic valves (stenosis, insufficiency, bicuspid) - mitral valves (stenosis, regurgitation) - Hypoplastic left heart syndrome|
|Other congenital malformations|
|Dextrocardia - Levocardia - Cor triatriatum|
|Great arteries||aorta (Patent ductus arteriosus, Aortic coarctation, Interrupted aortic arch, Overriding aorta, Aneurysm of sinus of Valsalva, Vascular ring) - Pulmonary atresia|
|Great veins||Persistent left superior vena cava - Total anomalous pulmonary venous connection - Scimitar syndrome|
|Other||Arteriovenous malformation (Cerebral arteriovenous malformation)|
|See also non-congenital conditions (I, 390-459)|