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Letterer-Siwe disease

Letterer-Siwe disease
Classification & external resources
ICD-10 C96.0
ICD-9 202.5
OMIM 246400
DiseasesDB 5906
MeSH D006646

Letterer-Siwe disease is a condition where histiocytes proliferate in the body. It is sometimes classified as a form of Langerhans cell histiocytosis, or as a diseminated form of histiocytosis X. It is most commonly seen in children less than two years old.

Additional recommended knowledge

Symptoms include lymphadenopathy, hepatosplenomegaly, and seborrhea-like lesions on the skin. Untreated, the disease is fatal. The five-year survival rate with treatment is fifty percent.

See also

This article is licensed under the GNU Free Documentation License. It uses material from the Wikipedia article "Letterer-Siwe_disease". A list of authors is available in Wikipedia.
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